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South African Journal of Surgery
versión On-line ISSN 2078-5151
versión impresa ISSN 0038-2361
Resumen
COETZEE, E y MALAKA, S. Malignant neuroendocrine tumour in an adult female diagnosed with Currarino syndrome. S. Afr. j. surg. [online]. 2019, vol.57, n.4, pp.9-13. ISSN 2078-5151. http://dx.doi.org/10.17159/2078-5151/2019/v57n4a3145.
Currarino syndrome is a rare, autosomal dominant condition of caudal anomalies, usually diagnosed in childhood. Adult presentation is rare and malignant transformation of the associated presacral mass even more so. We report a case of a 60-year-old female diagnosed with a malignant neuroendocrine tumour in the presacral mass in Currarino syndrome and describe the surgical management and pathological findings.